| Pulmonary capillary hemangiomatosis | |
|---|---|
| Other names | Wagenvoort syndrome |
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| Alveolar capillary proliferation as well as proliferation of larger blood vessels, probably venules. | |
| Specialty | Pulmonology |
Pulmonary capillary hemangiomatosis (PCH) is a disease affecting the blood vessels of the lungs, where abnormal capillary proliferation and venous fibrous intimal thickening result in progressive increase in vascular resistance.[1] It is a rare cause of pulmonary hypertension, and occurs predominantly in young adults.[2][3] Together with pulmonary veno-occlusive disease, PCH comprises WHO Group I' causes for pulmonary hypertension. Indeed, there is some evidence to suggest that PCH and pulmonary veno-occlusive disease are different forms of a similar disease process.[4]
- ^ Ortiz-Bautista, Carlos; Hernández-González, Ignacio; Escribano-Subías, Pilar (2017). "Enfermedad venooclusiva pulmonar y hemangiomatosis capilar pulmonar". Medicina Clínica (in Spanish). 148 (6). Elsevier BV: 265–270. doi:10.1016/j.medcli.2016.11.031. ISSN 0025-7753. PMID 28118962.
- ^ Masur Y, Remberger K, Hoefer M (1996). "Pulmonary capillary hemangiomatosis as a rare cause of pulmonary hypertension". Pathol Res Pract. 192 (3): 290–5, discussion 296–9. doi:10.1016/S0344-0338(96)80232-9. PMID 8739476.
- ^ El-Gabaly M, Farver CF, Budev MA, Mohammed TL (2007). "Pulmonary capillary hemangiomatosis imaging findings and literature update". J Comput Assist Tomogr. 31 (4): 608–10. doi:10.1097/01.rct.0000284393.76073.87. PMID 17882042. S2CID 35199069.
- ^ Lantu??joul, Sylvie; Sheppard, Mary N.; Corrin, Bryan; Burke, Margaret M.; Nicholson, Andrew G. (2006). "Pulmonary Veno-occlusive Disease and Pulmonary Capillary Hemangiomatosis". The American Journal of Surgical Pathology. 30 (7): 850–857. doi:10.1097/01.pas.0000209834.69972.e5. PMID 16819327. S2CID 25595167.